Abstract: The surgical treatment of Chiari malformation (CM) began in 1932. With the advance of medical technology, the surgical technique of CM is also in constant improvement. But due to its pathogenesis has not yet clear, there is no accepted optimal method, and different levels of the operation is still controversial. The author reviewed the concept, pathogenesis, diagnosis and surgical treatment of CM. The hot topics and new technological application were also reviewed in this article.

Key words: Arnold-Chiari malformation, Syringomyelia, Neurosurgical procedures, Review

摘要： Chiari畸形的外科治疗始于1932 年，70 余年来随着医学技术的不断进步，其手术方式不断改进。然而，由于发病机制至今尚未明确，致使不能形成一种临床公认的最佳外科手术方法，手术过程中不同层次的操作步骤或具体方法仍存有争议。本文拟就Chiari 畸形的概念、发病机制、诊断与神经外科手术治疗方法进行回顾，并对目前的热点问题和新技术应用进行概述。

关键词: Arnold-Chiari畸形, 脊髓空洞症, 神经外科手术, 综述