Clinical analysis of spinal hemangioblastoma: report of 7 cases with litertures review

doi:10.3969/j.issn.1672-6731.2020.10.011

Abstract

Abstract:

Objective To summarize the treatment experiences and surgical measure and efficacy of spinal hemangioblastoma. Methods and Results The surgical experiences of 7 patients with spinal hemangioblastoma from February 2012 to February 2017 in Tianjin Huanhu Hospital were analyzed retrospectively. Spinal MRI showed occupying lesion, empty vessel signals and syringomyelia (SM), with enhancement, All patients underwent microsurgical resection, and total resection was achieved (total excision in 5 cases and focus of responsibility total resection in 2 cases). Pathological examination confirmed hemangioblastoma. After operation, 6 cases improved, one case had no change, and no one died. During follow-up period, 5 cases was McCormick Scale Ⅰ, one was McCormick Scale Ⅱ, and one was McCormick Scale Ⅲ. No tumor recurrence was found. Conclusions The spinal hemangioblastoma is highly vascularized benign intramedullary tumors that can be cured surgically under microscopy.

Key words: Spinal cord neoplasms, Hemangioblastoma, Microsurgery

摘要：

目的总结脊髓血管母细胞瘤的治疗方法、疗效和临床经验。方法与结果 2012年2月至2017年2月共收治7例脊髓血管母细胞瘤患者，术前MRI显示脊髓占位明显、病灶周围血管流空影伴脊髓空洞症，病灶明显强化。经椎板切开行肿瘤切除术，手术全切除肿瘤（全切除5例、全切除责任病灶2例）；术后组织病理证实为血管母细胞瘤。术后运动和感觉功能改善6例、无变化1例；McCormick分级Ⅰ级5例、Ⅱ级1例、Ⅲ级1例；无肿瘤复发病例。结论脊髓血管母细胞瘤为高度血管化的良性髓内肿瘤，可经手术全切除治愈。脊髓血流分布异常可能是导致临床症状的原因之一。

关键词: 脊髓肿瘤, 血管母细胞瘤, 显微外科手术

WANG Huan-yu, WANG Hong, MA Quan-feng, TIAN Yuan. Clinical analysis of spinal hemangioblastoma: report of 7 cases with litertures review[J]. Chinese Journal of Contemporary Neurology and Neurosurgery, 2020, 20(10): 908-913.

王焕宇, 王宏, 马全锋, 田媛. 脊髓血管母细胞瘤七例临床分析[J]. 中国现代神经疾病杂志, 2020, 20(10): 908-913.

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