囊性嗜铬细胞瘤的诊断和治疗进展

基础医学与临床 ›› 2021, Vol. 41 ›› Issue (7): 1066-1070.

囊性嗜铬细胞瘤的诊断和治疗进展

杨庭楷, 文进^*, 纪志刚^*, 董德鑫, 叶子兴

中国医学科学院北京协和医学院北京协和医院泌尿外科, 北京 100730

收稿日期:2020-09-29 修回日期:2021-04-27 出版日期:2021-07-05 发布日期:2021-06-17
通讯作者: *wjpumch@163.com; jzgjxmc@163.com
基金资助:
中国医学科学院中央级公益性科研院所基本科研业务费临床与转化医学研究基金(2019XK320027); 外国文教专家项目管理基金(G20190001645)

Progress in diagnosis and treatment of cystic pheochromocytoma

YANG Ting-kai, WEN Jin^*, JI Zhi-gang^*, DONG De-xin, YE Zi-xing

Department of Urology, Peking Union Medical College Hospital, CAMS & PUMC, Beijing 100730, China

Received:2020-09-29 Revised:2021-04-27 Online:2021-07-05 Published:2021-06-17
Contact: *wjpumch@163.com; jzgjxmc@163.com

摘要/Abstract

摘要： 囊性嗜铬细胞瘤是非常罕见的神经内分泌肿瘤,大多无明显临床症状,术前经常不能被准确诊断。当影像学检查发现肾上腺区囊性占位时均应筛查囊性嗜铬细胞瘤的可能。目前最有效的治疗方式是手术切除,腹腔镜肾上腺切除术已成为首选术式,充分的术前准备和严密的术后监护是确保患者围手术期安全的重要前提。

关键词: 囊性嗜铬细胞瘤, 诊断, 外科手术

Abstract: Cystic pheochromocytoma is an uncommon neuroendocrine tumor, which mostly has no obvious clinical symptoms, and difficult to make correct diagnosis before surgical operation. When a cystic mass in the adrenal gland is found by imaging examination, the possibility of cystic pheochromocytoma should be screened. At present, the most curative treatment is surgical resection. Laparoscopic adrenalectomy is the first choice. Adequate preoperative preparation and strict postoperative monitoring are important pre-requisites for ensuring the safety of patients during the peri-operative period.

Key words: cystic pheochromocytoma, diagnosis, surgical operation

中图分类号:

R736.6

杨庭楷, 文进, 纪志刚, 董德鑫, 叶子兴. 囊性嗜铬细胞瘤的诊断和治疗进展[J]. 基础医学与临床, 2021, 41(7): 1066-1070.

YANG Ting-kai, WEN Jin, JI Zhi-gang, DONG De-xin, YE Zi-xing. Progress in diagnosis and treatment of cystic pheochromocytoma[J]. Basic & Clinical Medicine, 2021, 41(7): 1066-1070.

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