Abstract: Objective The type 1 autoimmune pancreatitis is gradually being recognized, but the type 2 AIP is still very rare in Asia. This paper summarizes the clinical characters of type-2 AIP patients in Peking union medical college hospital（PUMCH）.Methods From January 2001 to December 2016,all type 2 AIP hospitalized patients who met the ICDC were included in the study. The clinical data, laboratory results and imaging features of all patients were recorded, verified and follow-up. Results Six patients with type 2 AIP were included in the study. The ratio of men and women was 2/1, with an average age of 38.4 years. 67.7% (4/6) patients have UC. 37.7% (2/6) of patients were asymptomatic. Three patients were diagnosed by pathology. 50% (3/6) of patients showed mass of pancreas, and 50% (3/6) of patients showed pancreatic enlargement. Conclusions The clinical manifestations of the type 2 AIP patients in PUMCH are the same as those in foreign countries.

Key words: Key, Autoimmune pancreatitis, chronic pancreatitis, type 2 autoimmune pancreatitis ， type 1 autoimmune pancreatitis, swollen of pancreas, pancreatic duct stricture, pancreas placeholder, pancreatitis